Noj qab haus huvCov kab mob thiab mob

Antiphospholipid syndrome: ua zoo dev tom ntawm koj lub plawv nres

Antiphospholipid syndrome nyob rau hauv kev xyaum yog ib tug ntau dua ib txwm mus tsim cov ntshav txhaws nyob rau hauv cov leeg thiab nyob rau hauv cov hlab ntsha. Cov poj niam tej zaum tseem yuav qhov ncuav me nyuam tau.

Tej zaum cov syndrome yog tsis meej pem nrog lupus, tiam sis lawv tsis tas tam sim no nyob rau tib lub sij hawm. Antiphospholipid syndrome - ib qho kev ywj kab mob. Cov neeg mob feem ntau muaj mob thiab lupus, tiam sis feem ntau cov neeg mob tsis qhia tej yam cim ntawm nws los yog lwm kab mob autoimmune. Tam sim no, tus neeg mob yog txwv kom muab zais rau hauv cov neeg uas muaj lupus manifests nws tus kheej ua ke nrog rau cov syndrome, thiab cov neeg uas tsis tau pom zoo li. Txawm li cas los, qhov teeb meem yog tsis tsuas nyob rau hauv cov tshuaj tiv thaiv phospholipids, vim hais tias 5% yog tsis txom nyem los ntawm ib tug uas zoo sib xws tus kab mob muaj tshuaj.

Homeostasis yog, tswj lub constancy ntawm qhov chaw, nyob rau hauv particular, lub cev ntawm qhov nruab nrab. Feem ntau, cov ntshav txhaws yog khaws cia nyob rau hauv ib tug tej theem ntawm lub cev. Yog hais tias ib tug neeg suffers los ntawm ib tug kab mob "antiphospholipid syndrome", qhov hloov maj mam mechanisms yog ua txhaum. Txawm li cas los, thrombosis mechanisms yog tsis qoos taub. Tsuas muaj cov kev xav. Ib tug ntawm lawv - ib tug compound ntawm lub phospholipids ntawm cell week mus ntshav proteins uas ua rau "kuj zoo kawg xim" los ntawm cov tshuaj, txij li thaum cov khoom no mas txawv teb chaws mus rau hauv lub cev, thiab yog li ntawd yuav raug puas tsuaj. Qhov thib ob hypothesis - hais tias tus neeg mob lub cev ua cov tshuaj tiv thaiv cov yam tseem ceeb muab kev koom tes nyob rau hauv cov kev cai ntawm cov ntshav txhaws, namely prothrombin thiab tawm tsam tej yam kev proteins. Tsis tas li ntawd liam rau platelets thiab, noj nyias. Ib txhia neeg xav hais tias mus blame cov tshuaj tiv thaiv ntawm lub puab phab ntsa ntawm cov hlab uas ua rau platelets thiab monocytes ua raws li nws tus kheej thiab li ntxias thrombosis, uas muaj peev xwm tej zaum ua rau ib tug myocardial infarction.

Rau cov poj niam, thiab nce cov ntxhais hluas mus txog 40 xyoo, yog ntau cov yam ntxwv ntawm cov antiphospholipid syndrome. Cov tsos mob ntawm nws heev kaj, tsuas yog hais tias nws yog muaj ua ke nrog lupus. Txwv tsis pub, cov tsos mob yuav ua tau heev vague. Piv txwv li, tas mus li migraine, heev ntawm daim tawv nqaij, txo tus naj npawb ntawm cov ntshav platelets.

Yuav ua li cas los yog tshawb nrhiav qhov syndrome? Nrog kev pab los ntawm ib tug tshwj xeeb cov ntshav mus kuaj tshuaj rau phospholipids. Tej zaum cov neeg mob tau txais ib tug ntxiv rau lub Wassermann cov tshuaj tiv thaiv. Nws yog raws li yog hais tias nws yog neeg muaj mob nrog syphilis. Yog li ntawd, tus kws kho mob yuav tsum tau ceev faj nyob rau hauv kev mob. Tej zaum tus neeg mob muaj mob syphilis, thiab antiphospholipid syndrome. Kev kho mob ntawm xws cov neeg mob tau tsis yeej ib txwm tau nws yog dab tsi tam sim no: muaj cov evolution ntawm kev kho mob. Tam sim no, nws purports los mus tiv thaiv cov ntshav los khov rau ntawd, piv txwv li prescribers tiv thaiv txhaws. Tom qab tag nrho cov, nyob rau hauv no mob nws yog tshwj xeeb yog txaus ntshai ntshav txhaws. Yog li ntawd, cov neeg mob tau txais zookumarin thiab heparin, txawm hais tias lawv coj mus muag npe tej zaum yuav txawv nyob rau hauv ntau lub teb chaws. Tab sis nws yog heev haib anticoagulants. Tej zaum yam tshuaj nyob rau hauv qhov kev txiav txim aspirin tshuaj xaiv nyob rau hauv cov ntaub ntawv no yog me me. Tshuaj tiv thaiv muab prednisone, uas kuj yuav pab tau kom tsis txhob mob thiab tiv thaiv tus neeg mob los nres tshuaj tiv thaiv cell daim nyias nyias. Muaj lupus yog zoo heev girdroksihlorokin. Cev xeeb tub taw gamma globulin los tiv thaiv tus me nyuam. Txawm li cas los, tsis ntev los no kev tshawb fawb nws yog lub npe hu tias ua ke nrog ntawm heparin thiab cov tshuaj aspirin - ib tug ntau zoo tswvyim.

Yog li, qhov teebmeem ntawm cov kab mob autoimmune yuav cuam tshuam rau tej khoom hauv nrog cev ntawm tus txiv neej. Tshuaj li no rhuav tshem cov cell daim nyias nyias. ntshav txhaws yam tsis ua hauj lwm kom zoo - thiab tau cov ntshav txhaws. Nyob rau hauv txhua rooj plaub, xaiv ib tug tshwj xeeb tswvyim uas tso cai rau kom tshem tawm cov tsos mob. Yog hais tias koj cov tawv nqaij pib hloov xim vim nchuav menyuam, koj tsis tau dais lub cev xeeb tub, los sis mam li nco dheev ntawm ib tug hluas hnub nyoog uas koj tau muaj ib lub plawv nres - hu rau koj tus rheumatologist.

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