Harlequin Syndrome: Cov tsos mob, cov nta thiab kev kho mob

Me nyuam mos cov me nyuam mos yog heev lam tau lam ua. Txawm nyob rau hauv lub plab, lawv yuav muaj cuam tshuam los ntawm ntau yam tsis zoo yam tseem ceeb uas ua rau lub pathology ntawm tej yam khoom noj. Raws li ib tug tshwm sim, yug, tus me nyuam muaj ib tug ntau ntawm teeb meem. Ib tug ntawm cov phem tshaj txawv yog Harlequin syndrome. Tus kab mob yog muaj npe tom qab lub cim ntawm lub Italian commedia dell'arte, uas coj qhws ib ce ua los ntawm cov yeeb yuj ntaub scraps.

Harlequin syndrome nyob rau hauv cov me nyuam mos

Cov kws kho mob nrhiav cov teeb meem tam sim ntawd tom qab yug tus me nyuam ntawm ib tug me nyuam. Raws li lawv, cov Harlequin syndrome yuav piav los ntawm tus neeg txhaum ntawm lub autonomic system uas yog tsis muaj txoj cai los tswj vascular laus. Tus kab mob kuj yuav txhais los ntawm tej yam yooj yim lub ntiajteb txawj nqus. Yog vim li cas yog no mas? Cov kws kho mob yuav muab tsis tau ib tug ntshiab lus teb rau ceev cov lus nug. Cov kab kev los ntawm yog vim li cas rau lub dav heev: los ntawm tej yam yooj yim ua hauj lwm ntawm me nyuam hauv plab kev loj hlob rau cov neeg pluag kev ua neej xaiv, uas ua rau yus tus cev xeeb tub poj niam.

Lub syndrome yuav manifest raws li tag nrho cov thoob lub cev, thiab tsuas yog nyob rau hauv tej qhov chaw ntawm lub cev. Cov me nyuam, cov kws kho mob hais tias, yog tas li mob uas mob khaub thuas, vim hais tias lawv ntxhov thermoregulation. Me nyuam me ntawm txhua lub sij hawm ntawm lub xyoo yuav tawm hws profusely, ces dheev rau supercool, raws li ib tug tshwm sim ntawm tus kab mob pheej yog muab rau nws. Nyob rau hauv tas li ntawd, cov syndrome muab tsis xis nyob hnyav, li ntawd, feem ntau tus me nyuam quaj quaj, nws nyob tsis tswm thiab chim siab.

cov tsos mob

Raws li ib co lus ceeb toom, lub syndrome yuav ua tau ib tug rau txim ntawm me nyuam hauv plab asphyxia los yog tau lawv thaum yug los intracranial raug mob. Nws twb tseem paub hais tias nyob rau hauv tus neeg mob txhab ntawm lub hypothalamus thiab medulla oblongata. Nyob rau hauv txhua rooj plaub, lub tswv yim tam sim ntawd ua rau ib tug neurologist. Ntes tus kab mob yog yooj yim heev: nws yog ib lub ntsiab cov tsos mob ntawm liab ntawm daim tawv nqaij, thaum lub ib qho kuam me me dag rau ntawm nws sab. Nyob rau hauv cov ntaub ntawv no, tus ciam ntawm cov xim hloov yuav siv sij hawm qhov chaw raws nraim nyob rau hauv txoj kab ntawm cov nqaj qaum.

Sis tsis ncaj xim qhov chaw ntawm lub cev tshwm sim ib ob peb feeb tom qab ib tse nrog koj tus me nyuam. Nws zoo nkaus li raws li Harlequin syndrome. Diam duab me nyuam me me nyob rau hauv kev kho mob encyclopedias qhia cov dab tuag duab - lub sab sauv ib feem ntawm lawv lub cev muaj ib qho nqaij daim tawv, qhov pib yuav kaj liab, tej zaum nrog ib tug xiavlus zas. Cov tshwm sim yog hnov rau ob peb feeb. Ib txhia kws txawj hais tias cov syndrome tej zaum yuav ib tug kos npe rau ntawm prematurity.

cutaneous ces

Yog hais tias qhov kev piav qhia ntawm tus kab mob mus siv kho mob cov ntsiab lus, cov Harlequin syndrome manifests nws tus kheej raws li ib tug compact daim tawv nqaij keratinization. Nws tsis yog ib tug thiaj li hu ua granular txheej, es tsis txhob pom plaques tsim thaum lub sij hawm ntes ntawm lub epidermis. Cov formations muaj ib tug hexagonal zoo, lawv muaj feem ntau sib cais los ntawm sib sib zog nqus liab tej kab nrib pleb. daim tawv nqaij xim thaum gray los yog jaundiced.

Cov me nyuam yug los nrog rau qhov no syndrome feem ntau muaj lwm yam kev txawv txav: tej zaum lawv yuav tshwm sim deformation ntawm lub qhov ncauj (daim di ncauj nws nco ntsoov ntses), ectropion, tsis tsim ib yam nkaus thiab tiaj tus pob ntseg. Nyob rau hauv tej rooj plaub, mob microcephaly, thaum tus me nyuam yog underdeveloped pob txha taub hau: raws li ib tug tshwm sim, nws tau yug los nrog ib tug heev me me lub hlwb. Tej cov me nyuam tuag nyob rau hauv lub neonatal lub sij hawm los yog thaum yug los.

nta ntawm tus kab mob

Cov me nyuam yeej tsis tuag, yog hais tias lawv muaj lub pathology ntawm Harlequin. Lub syndrome tsis yog ib tug kab lus. Tus kab mob yuav tsis tau cov lus hais, dua li, yog hais tias nws yog sai sai kuaj thiab competently, yuav alleviate tus mob yam khoom noj tshwj xeeb npaj. Cov me nyuam no yog ua txhaum xwb tsis tshav kub, tab sis kuj cov ntsha tshuav nyiaj li cas. Chapped daim tawv nqaij utrudnyaet ua tsis taus pa thiab zog. Nyob rau hauv loj tej kab nrib pleb yuav tau txais tus kab mob no thiab tsim sepsis.

Qhov zoo ces, tus kab mob no yog tsis heev. Nyob rau hauv cov ntaub ntawv no, tus me nyuam mos kev sib deev koom tsis: lub pathology raug rau cov tub thiab cov ntxhais. Cov kws kho mob hais tias lub syndrome feem ntau sau ib qho nyuaj. Cov raug nyob rau hauv feem ntau txaus unfavorable. Lub aetiology ntawm lub syndrome yog tseem tsis paub hais tias.

txoj kev kho

Yam khoom noj tshuaj rau thaum kawg ntawm kev kho mob, uas aims kom muaj lub cev lub cev kub thiab stabilization ntawm dej-ntsha tshuav nyiaj li cas. Ntxiv mus, xws li ib tug neeg mob yuav tsum tau ib qho kev noj haus, antiinflammatory, antibacterial txoj kev kho. Kev siv cov retinoids nyob rau hauv daim ntawv ntawm cov tshuaj pleev thiab lub qhov ncauj tsiav tshuaj ho tsub kom cov ciaj sia taus tus nqi, yog tias tus me nyuam thiaj paub tias yog Harlequin syndrome. Kev kho mob yuav siv cov tshuaj, nyob qhov twg lub active tshuaj yog isotretinoin thiab acitretin. Dua li no, lub tsis xws luag nyob twj ywm rau ntawm daim tawv nqaij kom txog thaum lub kawg ntawm hnub. Qhov zoo tshaj ntawm lub neej nyob rau hauv cov neeg mob no ho txo.

Yog hais tias lub syndrome yog tsis hais, nws yog tau ua tsis tau tshuaj. Cov niam txiv txaus yug nyob rau hauv cov me nyuam me qub kub - nyob ib ncig ntawm 20 degrees. Qhia cov crumbs mus rau climatic extremes yuav tsum maj: xub thawj, nws yuav tsum hloov mus rau qhov txias, thiab xwb ces thaum tshav kub kub. Qhov no txoj kev koj yuav qhia cov autonomic system thiab lub phab ntsa kas hlab ntsha. Nco ntsoov: Yog hais tias tus me nyuam twb tawm hws, koj yuav tsum hloov khaub ncaws tam sim ntawd. Tej txheej txheem yuav tsum tau muab ib tug zoo tshwm sim.